Ahụ ikeỌrịa na ọnọdụ

Ehlers Danlos ọrịa,

Ehlers-Danlos syndrome - kasị nkịtị ketara
connective anụ ahụ ọrịa. The omume bụ onye ikpe
a narị puku mụrụ ọhụrụ. N'okpuru a syndrome jikọtara otu
ọrịa nke na-dabere na ntụpọ collagen nke Nleta ndabere
connective anụ ahụ. Ọ nyere ihe karịrị iri ụdị ọrịa, dị iche iche n'akụkụ ụfọdụ. Mpụga ịrịba ama na-nwere Ehlers-Danlos syndrome, kwupụtara na ụba extensibility, anụ vulnerability, agagharị nke nkwonkwo na mgbaàmà nke hemorrhagic diathesis. E nwekwara mmeri nke akụkụ okuku ume na usoro na obi usoro, nweekwa usoro, eriri afọ tract.

The akpụkpọ nke ọrịa na a nchoputa nke Ehlers Danlos syndrome, na-emebi emebi, na mkpa, agụghị oké ofu aka akpata arọ. Na nwetụrụ mmerụ nke anụ lacerations hardhealed ime, na saịtị ebe n'ichihịa kpụrụ na a wrinkled n'elu. Ọrịa Ehlers -Danlosa ji ndiiche agagharị nke nkwonkwo, nke bụ n'ihi nke-adịghị ala ala dislocations na subluxations nke nkwonkwo. Ọtụtụ mgbe ọrịa na-esonyere hemorrhagic diathesis, na ọrịa na mfe ichihịa na hematoma apụta dị iche iche orunótu. Ahụkarị ọbara ọgbụgba si eriri afọ tract, na-agazu n'agbụ, akpanwa.

N'ihi na ụfọdụ ụdị ọrịa na-ji retinal detachment na anya mmiri
eyeballs. Ehlers syndrome - Danlos syndrome mgbe ụfọdụ so na-ezighị ezi
guzobe ezé na ele mmadụ anya n'ihu na-anọghị, mmepe nke periodontitis.
Imebi nke nweekwa usoro na-egosipụta ụdị deformation nke obi
sel spinal curvature. Ọrịa na-emekarị hụrụ hainia
dị iche iche orunótu. Na mmeri nke esịtidem akụkụ-ata ahụhụ obi
arịa, bronchopulmonary usoro, vaskụla aneurysms ii multiple
ụbụrụ na aorta. Na mmeri nke obi na-guzobere iche iche omume ọjọọ.

Ehlers-Danlos ọrịa Ọgwụgwọ

Nnyocha dịgasị iche iche rụrụ maka ezi nchoputa nke ọrịa na
pụrụ iche inpatient ụlọ ọrụ. Weta oké ihe isi ike
obstetric na ịwa ahụ na nsogbu na-ọrịa ndị a chọpụtara na syndrome
Ehlers-Danlos syndrome. Ọgwụgwọ na-eduzi isi na stabilization na
normalize metabolic Filiks ke Central ụjọ usoro na obi usoro,
locomotor usoro. Agwọ maka ọrịa a na-agụnye
ịnabata a dịgasị iche iche nke vitamin B, A na E. Good pụta enye
carboxylase na ascorbic acid, injections nke ibu hormone (somatotropin
hormone) carnitine chloride. Ọrịa na-atụ aro ọgwụ na welie ụbụrụ ọrụ (Pantogamum, Nootropilum, Riboxinum, rutin, Pananginum). E wezụga na ọ dị mkpa ka jide ndị dị otú ahụ mgbe nile physiotherapy agwọ ọrịa dị ka laser igba okpukpu, magnetik ọgwụ. Ọrịa nwekwara nye iwu ọmụmụ nke physiotherapy na ịhịa aka n'ahụ, reflexology sessions.

Na ọgwụgwọ nke ọrịa nke oké anya ga-akwụ ụgwọ iji adịghị ala ala foci
ọrịa dị na ọnụ na nasopharynx (adenoids, ala ala
tonsillitis, Sinusitis, carious ezé). Special agwọ ọrịa maka syndrome ruo mgbe
Ọ bụghị e mepụtara. Na-atụ aro nnabata nwayọọ ụzọ ndụ na otú
kwere omume mgbochi ahụ ibu. Symptomatic ọgwụ na-agụnye ịwa mgbazi nke thoracic deformities, mwepụ pseudotumour, ọgwụgwọ nke anya pathologies, obi, wdg Amụma maka ndụ na-adabere n'ụzọ dị ukwuu na ụdị syndrome. Mgbochi bụ mkpụrụ ndụ ihe nketa ndụmọdụ.

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