Frehley syndrome: nkọwa, nchoputa, ọgwụgwọ, afọ ime na ịmụ nwa

Anomalies metụtara na urinary tract na akaụntụ maka n'elu 35% niile congenital malformations mmadụ. Na nke a, e nwere otu ebe dị otú ahụ na ọrịa na-asymptomatic ma kpebisie ike na naanị n'oge ah u ma ọ bụ ime. Frehley syndrome - akụrụ congenital anomaly agwa na nke a ngafe nke n'ihu ma n'azụ elu alaka nke gbasara akụrụ akwara. Dị ka a na ya pụta, disrupts nkịtị ahu ọrụ.

Aha nke syndrome aha mgbe ihe American urologist, onye mbụ kọwara ya. N'isiokwu a, anyị ga-agakwuru na ndị na-akpata, ihe mgbaàmà na ọgwụgwọ nke ọrịa.

Gịnị ka ọ bụ?

Dị ka ekwuola, ma ọ bụrụ na syndrome Frehley gafere n'ihu ma n'azụ alaka nke gbasara akụrụ akwara. Ọ bụ omume na-ele mmadụ anya n'ihu mkpakọ nke elu akụkụ nke pelvis ma ọ bụ ureteropelvic nkwụsị. Dị ka a n'ihi nke ọrụ nke akụrụ nwere ike imebi ma ọ bụ ọbụna na-efu. E nwere ohere nke nkume guzobere, ọdịdị nke ọbara mgbali. The mmamịrị nwere ike achọpụtara metụtara nke ọbara.

A yiri anomaly emee ọbụna n'oge embryogenesis gbasara akụrụ vaskụla usoro mgbe nwere ike ịkwụsị ha mmepe, ma ichebe owuwu.

Frehley syndrome na-metụtara nanị akụkụ ụfọdụ na n'aka nri na n'aka ekpe, ya bụ, ọ na-emekarị na-emetụta onye akụrụ. Na oké ikpe nwere ike na-ata ahụhụ ma na ozu. Mgbe a syndrome nwere ike so ntụpọ ejuputa na elu otu iko na nri ma ọ bụ n'aka ekpe pyeloectasia ruru ureteral mgbochi.

mgbaàmà

E nwere ụfọdụ ihe ịrịba ama n'ụzọ na-egosi na ọrịa nwere ike ịbụ Frehley syndrome. Mgbaàmà ndị kwesiri ngosi mgbu na lumbar region, gbasara akụrụ colic, nke nọ na njikọ na a abụọ nephrolithiasis. Ke adianade do, bụ obere ọbara mgbali elu, nakwa dị ka macro- na microscopic hematuria.

nchoputa nke syndrome

Ndị kasị sie ike ịchọpụta clinically Frehley syndrome na-eto eto, karịsịa na ụmụ ọhụrụ. Iji a ziri ezi nchoputa eji usoro nke Doppler gbasara akụrụ ọbara arịa, na-eji multislice agbakọrọ tomography.

Kids siri ike mepụta angiographic ọmụmụ, ya mere ha na-now na o siri ike na-eji.

Tụkwasị na nke a ụzọ nke ndị ọrịa kenyere ndị chịliri aka elu nke mmamịrị na ọbara ule, tinyere uche na ọgwụ ọjọọ na osisi. Ke adianade do, mepụta ultrasound nke urinary usoro.

therapies

Ọgwụgwọ nke ọrịa a na-kenyere nanị mgbe ịkpachara anya mgbagwoju nnyocha na nkwenye nke nchoputa. Conservative usoro - antihypertensive ọgwụ - eji na obere okwu. Ọ na-eduzi, dị ka a na-achị, a ọnụ ke mgbali ọ bụrụ na ọ na-akpọlite. Ọzọkwa na-eduzi a usoro nke jikoro iwepụ sekọndrị pyelonephritis na aku mgbochi nke urolithiasis.

Otú ọ dị, ụzọ kasị mma isi wepụ Frehley syndrome - ọgwụgwọ bụ mgbanwe na-awa ahụ. N'oge awa ahụ, dọkịta na-ewepu ịgafe nke akwara na akụrụ na nsogbu na ha na-kwụsị.

Na nke ọ bụla, ndị ọrịa na (karịsịa ụmụ) ga-ịdenyere aha na-nephrologist dọkịta mgbe nile ma na-ndụmọdụ ya, na-na ọ dị mkpa ule rue, ultrasonic na radiographic ọmụmụ. Na mgbe e mesịrị ndụ Frehley syndrome nwere onwe ya nnọọ na-adịghị egosi ogo erughị ala-adabere na otú ike clamped gbasara akụrụ pelvis. Na a ike ndụ na enweghị àgwà ọjọọ, ọrịa nwere ike na-eche ọ bụla mgbaàmà.

ime

Pregnancy na ọmụmụ nke a na nwa na syndrome Frehley nne ya nakwere nanị n'okpuru nlekọta nke a ọkachamara. A, ndị inyom na congenital akụrụ mmepe, nke na-agụnye nọ n'ọrụ syndrome, kwere na-amị mkpụrụ nanị mgbe ịwa ahụ. The eziokwu na Frehley si syndrome na-esokarị site na ọbara mgbali elu, afọ ime a na ikpe bụ ihe siri ike, mgbe ụfọdụ na ọ nwere na-etre na oge mgbe 22 izu.

Ma ọbụna mgbe a ọma ime ihe na mgbake nke gbasara akụrụ ọrụ nke ime nwaanyị kwesịrị igosi ya obstetrician. The dum oge nke gestation nke nwa ndidi a choro iji na-achị a nephrologist, site n'oge ruo n'oge maka ule, ọmụmụ na-ebe na, ma ọ bụrụ na ọ dị mkpa, ụlọ ọgwụ.

Ọtụtụ mgbe na-akawanye njọ gbasara akụrụ ọrịa nwere ike ime na oge nke 15-16 ma ọ bụ 26-30 izu. Ịrịba ama ndị kemwepu oge mmamịrị, oké ọzịza nke aka na ụkwụ, ihe mgbu na ahụ erughị ala n'oge urination. Na a gasịrị ụbọchị nsogbu bụ na o kwere omume n'ihi na ngwa ngwa na-eto eto akpanwa, nke na-ewepụta nsogbu na ureters. N'ihe banyere ndị dị otú ahụ ihe ịrịba ama nke afọ ime syndrome Frehley mkpa ngwa ngwa ụlọ ọgwụ.

Na-amụ nwa na syndrome Frehley

Ọtụtụ mgbe, akụrụ ntụpọ bụ ihe na-egosi caesarean ngalaba. Ma iyi egwu nwa na nke a bụ negligible.

N'ihi na ndị inyom na syndrome Frehley na ndị ọzọ na abnormalities nke akụrụ, e nwere pụrụ iche onodu n'ụlọ ọgwụ dị na steeti nke bụ mgbe nile urology na nephrology, na nwa ọhụrụ ozugbo ọmụmụ a rụrụ a mbara nnyocha e mere.

Ya mere, isiokwu e weere a ọrịa akụrụ ka Frehley si syndrome. N'agbanyeghị eziokwu na ndị anomaly bụ a congenital, ugbu a, ọ nwere ike a na-emeso nke ọma, na ndị ọrịa mgbe ịwa ahụ nwere ike laghachi a nkịtị si ebi ndụ.