Ahụ ikeỌrịa na ọnọdụ

Clinic Frederick syndrome

Frederick syndrome nwetara aha ya na nsọpụrụ nke Belgium physiologist, onye kọwaa ya dị ka a zọpụta nke a full transverse (atrioventikulyarnoy) mgbochi na atrial fibrillation, na ndị ọzọ - atrial flutter. Isiokwu a tụlere Frederick syndrome: adakarị atụmatụ, na ịgwọ ọrịa.

syndrome usoro

Frederick syndrome-esonụ usoro: si atria na ventricles kpamkpam akwụsị conduction nke gboo; agazi, jupụtara, mgbe mgbe, ugboro ugboro mmalite na Mbelata ụfọdụ iche iche nke muscle emep uta eri nke atria. The ventricles na-ụtọ site pacemaker, emi odude ke atrioventricular njikọ ma ọ bụ conduction usoro.

Ihe Kpatara Frederick syndrome

The ọrịa nwere ike ime mgbe oké organic ọnya nke obi, nke na-emekarị so site mkpali Filiks, sclerotome ma ọ bụ mbelata na myocardium. Ndị dị otú ahụ Filiks-agụnye ihe atụ, ischemic ọrịa obi, ọrịa na-akasị na ụdị adịghị ala ala, nnukwu myocardial infarction, myocarditis, cardiomyopathy, rịaworo pectoris na ndị ọzọ. Na ndị a ọrịa obi muscle ịzụlite sclerotic Filiks, n'ihi na isi kọwakwuru connective anụ, nke na-anọchi nke nkịtị, na-emebu mkpụrụ ndụ nwere ike na-eduzi ọkụ gboo. Ya mere, conductance na-akwusila, na e nwere mgbochi.

Nso ke cardiogram

Iji gosi na ọrịa syndrome Frederick, dị ka a na-achị, omume electrocardiograms ndinọ. Ọzọkwa, a na-amụ rụrụ maka mma ụbọchị iji chọpụta ihe ndị obi ọnụego n'oge dị iche iche na-anakọta ozi ndị ọzọ.

Na ọnụnọ nke ọrịa na ECG mmiri na ebili mmiri na-dere fibrillation ma ọ bụ atrial flutter, mgbe onye ahụ gbasiri ike ga nwere ezé. Ventricular n'afọ iri na ụma na-aghọ a ehiwe ma ọ bụ idioventricular, na n'ozuzu - nesinusovym ectopic. RR etiti oge na-mgbe nile na-enwe nri n'afọ iri na ụma. The ọnụ ọgụgụ nke ventricular ọnụego dekọrọ na ego adịghị nnọọ 50-60 ugboro kwa nkeji. Ventricular okụre bụ mgbe ikpọ na oruru.

Clinical ihe ịrịba ama na ihe mgbaàmà

Bụ nanị site n'enyemaka nke ihe ngwá nwere ike n'ụzọ ziri ezi na-akwado onye ọrịa Frederick syndrome. Clinic, so ya na-adị kwa ụbọchị ndụ, bụ nke a ịdọta uche nke onye - ọ bụ obere, ma nri obi ọnụego na a obi ọnụego nke dịkarịa ala 30 na-adịghị karịa 60 ugboro kwa nkeji. Usu ọnụego tụlee n'ihi belata pumping ọrụ nke obi. N'aka nke ya, na n'elu-eduga ná oxygen agu nke ụbụrụ.

Ọrịa ukwuu n'ime mkpesa nke adịghị ike, dizziness, mkpụmkpụ nke ume, na-akawanye njọ nke ahụ ike ọbụna mgbe a obere mmega. Ọ bụrụ na mmadụ anaghị ntị Frederick si syndrome, mgbaàmà na-aggravated, nwere ike iyi gbasara obi njide na-adịgide adịgide 5-7 sekọnd. Ke adianade do, e nwere ike ịbụ na ọnwụ nke nsụhọ n'ihi ventricular tachycardia.

ọgwụgwọ

Esiwanye, ndị dọkịta na-ekweta na naanị ezi ihe ngwọta maka ọgwụgwọ nke Frederick syndrome bụ nkunye nke keakamere pacemaker. Nke a na-etinyere n'ime ventricle electrode, nke na-anapụta pulses na artificially akpata mkpi nke myocardium. The ugboro ole nke mkpi atọrọ n'ọdịnihu dabere na ọnọdụ nke onye ọrịa na ya emega ahụ.

Ke adianade pacing na iji holinoblokatory. Nke a pụrụ iche ihe onwunwe, dị ka atropine. Nso nso a, Otú ọ dị, ha ngwa jụrụ n'ihi na nke ọtụtụ mmetụta, tinyere a na-ezighị ezi mmetụta na psyche onye ọrịa, n'ihi na ihe atụ, mmepe nke atropinovogo psychosis.

Ke ofụri ofụri, omume na-adabere na nkwụsi ike nke hemodynamics na-akpata atrioventikulyarnoy mgbochi.

N'ihi ya, Frederick syndrome bụ oké ezu imeri gbasara obi muscle, ji ngụkọta transverse mgbochi na Nchikota na atrial fibrillation.

Ugbu a, Otú ọ dị, na kwesịrị ekwesị na-adọ diagnoses a onu nwere ike a na-emeso, mgbe nke onye ọrịa nwere ike laghachi nkịtị na ịnọgide na-enwe ha omenala ụzọ ndụ.

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