Ahụ ike, Ọrịa na ọnọdụ
Clinic Frederick syndrome
Frederick syndrome nwetara aha ya na nsọpụrụ nke Belgium physiologist, onye kọwaa ya dị ka a zọpụta nke a full transverse (atrioventikulyarnoy) mgbochi na atrial fibrillation, na ndị ọzọ - atrial flutter. Isiokwu a tụlere Frederick syndrome: adakarị atụmatụ, na ịgwọ ọrịa.
syndrome usoro
Frederick syndrome-esonụ usoro: si atria na ventricles kpamkpam akwụsị conduction nke gboo; agazi, jupụtara, mgbe mgbe, ugboro ugboro mmalite na Mbelata ụfọdụ iche iche nke muscle emep uta eri nke atria. The ventricles na-ụtọ site pacemaker, emi odude ke atrioventricular njikọ ma ọ bụ conduction usoro.
Ihe Kpatara Frederick syndrome
The ọrịa nwere ike ime mgbe oké organic ọnya nke obi, nke na-emekarị so site mkpali Filiks, sclerotome ma ọ bụ mbelata na myocardium. Ndị dị otú ahụ Filiks-agụnye ihe atụ, ischemic ọrịa obi, ọrịa na-akasị na ụdị adịghị ala ala, nnukwu myocardial infarction, myocarditis, cardiomyopathy, rịaworo pectoris na ndị ọzọ. Na ndị a ọrịa obi muscle ịzụlite sclerotic Filiks, n'ihi na isi kọwakwuru connective anụ, nke na-anọchi nke nkịtị, na-emebu mkpụrụ ndụ nwere ike na-eduzi ọkụ gboo. Ya mere, conductance na-akwusila, na e nwere mgbochi.
Nso ke cardiogram
Iji gosi na ọrịa syndrome Frederick, dị ka a na-achị, omume electrocardiograms ndinọ. Ọzọkwa, a na-amụ rụrụ maka mma ụbọchị iji chọpụta ihe ndị obi ọnụego n'oge dị iche iche na-anakọta ozi ndị ọzọ.
Na ọnụnọ nke ọrịa na ECG mmiri na ebili mmiri na-dere fibrillation ma ọ bụ atrial flutter, mgbe onye ahụ gbasiri ike ga nwere ezé. Ventricular n'afọ iri na ụma na-aghọ a ehiwe ma ọ bụ idioventricular, na n'ozuzu - nesinusovym ectopic.
Clinical ihe ịrịba ama na ihe mgbaàmà
Bụ nanị site n'enyemaka nke ihe ngwá nwere ike n'ụzọ ziri ezi na-akwado onye ọrịa Frederick syndrome. Clinic, so ya na-adị kwa ụbọchị ndụ, bụ nke a ịdọta uche nke onye - ọ bụ obere, ma nri obi ọnụego na a obi ọnụego nke dịkarịa ala 30 na-adịghị karịa 60 ugboro kwa nkeji. Usu ọnụego tụlee n'ihi belata pumping ọrụ nke obi. N'aka nke ya, na n'elu-eduga ná oxygen agu nke ụbụrụ.
Ọrịa ukwuu n'ime mkpesa nke adịghị ike, dizziness, mkpụmkpụ nke ume, na-akawanye njọ nke ahụ ike ọbụna mgbe a obere mmega. Ọ bụrụ na mmadụ anaghị ntị Frederick si syndrome, mgbaàmà na-aggravated, nwere ike iyi gbasara obi njide na-adịgide adịgide 5-7 sekọnd. Ke adianade do, e nwere ike ịbụ na ọnwụ nke nsụhọ n'ihi ventricular tachycardia.
ọgwụgwọ
Esiwanye, ndị dọkịta na-ekweta na naanị ezi ihe ngwọta maka ọgwụgwọ nke Frederick syndrome bụ nkunye nke keakamere pacemaker. Nke a na-etinyere n'ime ventricle electrode, nke na-anapụta pulses na artificially akpata mkpi nke myocardium.
Ke adianade pacing na iji holinoblokatory. Nke a pụrụ iche ihe onwunwe, dị ka atropine. Nso nso a, Otú ọ dị, ha ngwa jụrụ n'ihi na nke ọtụtụ mmetụta, tinyere a na-ezighị ezi mmetụta na psyche onye ọrịa, n'ihi na ihe atụ, mmepe nke atropinovogo psychosis.
Ke ofụri ofụri, omume na-adabere na nkwụsi ike nke hemodynamics na-akpata atrioventikulyarnoy mgbochi.
N'ihi ya, Frederick syndrome bụ oké ezu imeri gbasara obi muscle, ji ngụkọta transverse mgbochi na Nchikota na atrial fibrillation.
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