Ahụ ike, Ọrịa na ọnọdụ
Hemolytic-uremic syndrome - ihe ọ bụ?
Hemolytic uremic syndrome bụ ihe mgbaàmà, nke na-egosipụta na ụdị hemolytic anaemia, OPN na thrombocytopenia. N'ihi na oge mbụ ọrịa a kọwara na 1955. Dị ka ndị ọkachamara, banyere 70% nke ikpe nchoputa na umu n'afọ mbụ nke ndụ, na nanị ole na ole mere e dere na ndị okenye. Ke ibuotikọ emi anyị ga-ekwu banyere nke a ọrịa, na-ele anya na otú a na-emeso site na oge a na ụzọ nke hemolytic uremic syndrome.
Immediate akpata
Mmepe nke a na ọrịa ndị ọkachamara na ugbu a na-ejikọta ya na ọtụtụ ihe. N'ụzọ bụ isi a malitere ịrịa na-egbu egbu mmebi capillary endothelium otú akpọ glomeruli. N'aka nke ọzọ kpatara ya nwere ike na-edina na DIC na n'ibu mmebi erythrocytes. Ọ na-kweere na nke ikpeazụ nwere ike mebiri emebi n'oge Itie site capillaries nke glomeruli onwe ha, nke bụ na n'aka jupụtara fibrin egbochi mkpụkọ.
isi mgbaàmà
Hemolytic-uremic syndrome emee predominantly na ụmụaka na a ngwa ngwa ọnụ ke mmamịrị mmepụta, ma na-anọghị nke doro anya ihe ịrịba ama nke akpịrị ịkpọ nkụ na na ndabere nke dịtụ nkịtị VEO kwa. Ọ bụrụ na a na nwa nwere a fever ma ọ bụ vomiting pụtara yikarịrị ọrịa na-aga n'ihu ngwa ngwa - enwere a ụbụrụ edema. Ọtụtụ mgbe, hemolytic uremic syndrome na-complemented ọtọ-gbaa ya akpụkpọ nwa, na obere okwu, na obere eruptions.
Ịchọpụta Otú Nsogbu
Iji gosi ndị dị otú ahụ a nchoputa ka hemolytic-uremic syndrome, ị ga-agafe a usoro nke ule, tinyere zuru ọbara analysis. Naanị mgbe a zuru nnyocha nke onye ọrịa nwere ike ikwu banyere ihe ọzọ ọgwụgwọ.
Modern ụzọ nke ọgwụgwọ
More na nso nso nyere nchoputa enwe nnọọ elu (80 100%). Otú ọ dị, ndị ọkà mmụta sayensị na-mgbe niile na-achọ a ngwọta na-nsogbu a. N'ihi ya, ọ e kere ngwaọrụ akpọ "wuru akụrụ", ekele nke ọnọdụ gbanwere radically. Taa, ọnwụ fọrọ nke nta mgbe ime (n'etiti abụọ na iri percent). Ha nwere ike ịbụ nanị n'oge mbubreyo ọrịa nchọpụta, nakwa dị ka na mmepe nke irreversible Filiks na ụbụrụ ruru ya ọzịza. Ọ ga-kwuru na ndị dị otú nchoputa bụ gbara gharịị hemolytic uremic syndrome, n'ozuzu na-achọ si 2 to 9 sessions (kwa ụbọchị) iji "wuru akụrụ". Site na nke a dialysis ọkachamara nwere ike ịnọgide na-enwe kwesịrị etoju nke metabolites, nakwa dị ka gbochie ụbụrụ ọzịza.
ele ihe anya
Modern ụzọ ekwe ụmụaka aka idi nsogbu a. Otú ọ dị, nke a bụ omume na naanị na ihe omume na ọrịa e achọpụtara ya mbụ nkebi. Ma ọ bụghị ya, na likelihood nke n'ụzọ zuru ezu naghachi dịtụ ala. Dị ka ndị ọkachamara, ọnọdụ na-anọghị nke a nke oma omume na akụkụ niile nke ahụ mgbe 2-3 sessions nke hemodialysis, amụma nnọọ ọjọọ.
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